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Cranial MRI changes may precede symptoms in Hallervorden-Spatz syndrome

  • Susan J. Hayflick
  • , Johann M. Penzien
  • , Wolfgang Michl
  • , Uzma M. Sharif
  • , N. Paul Rosman
  • , Patricia G. Wheeler

Research output: Contribution to journalArticlepeer-review

Abstract

Two families are presented in which siblings of children affected with Hallervorden-Spatz syndrome exhibited characteristic cranial magnetic resonance imaging changes before developing clinical features of the disease. Linkage to a major locus on chromosome 20p supported the diagnosis of Hallervorden-Spatz syndrome. In some patients with Hallervorden-Spatz syndrome, iron is radiographically evident before the onset of clinical symptoms.

Original languageEnglish (US)
Pages (from-to)166-169
Number of pages4
JournalPediatric Neurology
Volume25
Issue number2
DOIs
StatePublished - 2001

Funding

The authors thank the families with Hallervorden-Spatz syndrome, without whom this study could not have been performed. A. Malone and S. Bae provided valuable technical assistance. This work was supported in part by NIH grants 1R01 EY12353 and 5K23 EY00348 to SJH.

FundersFunder number
Author National Institutes of Health National Institutes of Health National Institutes of Health National Institutes of Health The Bev Hartig Huntington's Disease Foundation National Institutes of Health5K23 EY00348
National Eye Institute and Casey Eye InstituteR01EY012353

    ASJC Scopus subject areas

    • Pediatrics, Perinatology, and Child Health
    • Neurology
    • Developmental Neuroscience
    • Clinical Neurology

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