Intraosseous malignant peripheral nerve sheath tumor in a patient with neurofibromatosis

David G. Terry, Donald D. Sauser, Melissa D. Gordon

Research output: Contribution to journalArticlepeer-review

22 Scopus citations


Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon sarcomas that almost always arise in soft tissue. They can develop in pre-existing neurofibromas or schwannomas, de novo from peripheral nerves, or following radiation therapy. Primary intraosseous MPNST is rare and has been reported most frequently in the mandible. Of the reported cases involving the long bones, none has been associated with neurofibromatosis type 1 (NF-1). We report a case of MPNST arising in the femur in a patient with NF-1.

Original languageEnglish (US)
Pages (from-to)346-349
Number of pages4
JournalSkeletal Radiology
Issue number6
StatePublished - Jun 1998
Externally publishedYes


  • Bone
  • Malignant peripheral nerve sheath tumor
  • Neurofibromatosis

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging


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