Abstract
Papillon-Lefèvre syndrome (PLS) is a rare inherited palmoplantar keratoderma (PPK) that is associated with progressive gingivitis and recurrent pyodermas. We present a case exhibiting classic features of this autosomal-recessive condition and review the current understanding of its pathophysiology, diagnosis, and treatment. Additionally, a review of pertinent transgredient PPKs is undertaken, with key and distinguishing features of each syndrome highlighted.
Original language | English (US) |
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Pages (from-to) | 193-198 |
Number of pages | 6 |
Journal | Cutis |
Volume | 93 |
Issue number | 4 |
State | Published - Apr 2014 |
Externally published | Yes |
ASJC Scopus subject areas
- Medicine(all)