Association of pulmonary artery agenesis and hypoplasia of the lung

Renato Vitiello, Chiara Pisanti, Antonello Pisanti, Michael Silberbach

Research output: Contribution to journalArticlepeer-review

9 Scopus citations


Pulmonary artery agenesis and hypoplasia of the homolateral lung occasionally occurs as an isolated lesion, but more often has associated congenital cardiac anomalies. We present a case where pulmonary artery agenesis was the sole lesion in an asymptomatic child. Pulmonary artery agenesis should be suspected in asymptomatic patients if a plain chest X-ray shows asymmetric lung fields, lung hypoplasia, or hyperinflation of the contralateral lung. Echocardiography is the best tool to establish the diagnosis. In our opinion, invasive procedures, such as cardiac catheterization, may be postponed if there is no echocardiographic evidence of pulmonary hypertension.

Original languageEnglish (US)
Pages (from-to)897-899
Number of pages3
JournalPediatric pulmonology
Issue number9
StatePublished - Sep 2006


  • Dyspnoea
  • Exercise tolerance
  • Hemoptysis
  • Lung hypoplasia
  • Lung infections
  • Pulmonary artery agenesis
  • Pulmonary edema
  • Pulmonary function testing
  • Pulmonary hypertension

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Pulmonary and Respiratory Medicine


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