TY - JOUR
T1 - Fasciitis in amyopathic dermatomyositis
AU - Allen, Everett
AU - Schmahmann, Sandra
AU - Sauser, Don
AU - Barkhuizen, André
N1 - Copyright:
Copyright 2021 Elsevier B.V., All rights reserved.
PY - 2003/2
Y1 - 2003/2
N2 - Dermatomyositis is a disease frequently treated by rheumatologists and dermatologists due to prominent systemic features of inflammatory myositis, less common arthritis, and rare systemic vasculitis, in addition to the characteristic cutaneous manifestations of Gottron's papules over extensor surfaces, and a heliotrope rash over the eyelids. Patients with amyopathic dermatomyositis, a subset of dermatomyositis, display skin disease but no apparent muscle disease. This report describes an adult patient with the typical dermatomyositis rash with no weakness, normal muscle enzymes, and the unique finding of fasciitis without myositis on muscle biopsy, which correlated with a Magnetic Resonance Imaging (MRI) finding of a peripheral halo of intense signal around muscles on T2-weighted and fat suppression sequences. Although MRI finding of presumed fasciitis has been reported in juvenile-onset dermatomyositis, this is the first report of MRI evidence of fasciitis with pathological correlation in adult-onset dermatomyositis. We suggest that if MRI scans are ordered, as part of the work-up of dermatomyositis, a peripheral halo of increased signal should specifically be looked for, which could be interpreted as fasciitis based on this case report.
AB - Dermatomyositis is a disease frequently treated by rheumatologists and dermatologists due to prominent systemic features of inflammatory myositis, less common arthritis, and rare systemic vasculitis, in addition to the characteristic cutaneous manifestations of Gottron's papules over extensor surfaces, and a heliotrope rash over the eyelids. Patients with amyopathic dermatomyositis, a subset of dermatomyositis, display skin disease but no apparent muscle disease. This report describes an adult patient with the typical dermatomyositis rash with no weakness, normal muscle enzymes, and the unique finding of fasciitis without myositis on muscle biopsy, which correlated with a Magnetic Resonance Imaging (MRI) finding of a peripheral halo of intense signal around muscles on T2-weighted and fat suppression sequences. Although MRI finding of presumed fasciitis has been reported in juvenile-onset dermatomyositis, this is the first report of MRI evidence of fasciitis with pathological correlation in adult-onset dermatomyositis. We suggest that if MRI scans are ordered, as part of the work-up of dermatomyositis, a peripheral halo of increased signal should specifically be looked for, which could be interpreted as fasciitis based on this case report.
KW - Amyopathic dermatomyositis
KW - Erythematous rash
KW - Magnetic resonance imaging
KW - Pruritic rash
UR - http://www.scopus.com/inward/record.url?scp=0037326123&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=0037326123&partnerID=8YFLogxK
U2 - 10.1097/01.RHU.0000049716.25111.AF
DO - 10.1097/01.RHU.0000049716.25111.AF
M3 - Article
C2 - 17041424
AN - SCOPUS:0037326123
SN - 1076-1608
VL - 9
SP - 51
EP - 53
JO - Journal of Clinical Rheumatology
JF - Journal of Clinical Rheumatology
IS - 1
ER -