Renal Lymphangiectasia in a Pediatric Patient

Sudhen B. Desai; Raphael C. Sun; Brittany L. Johnson; Kristy L. Rialon; Ionela Iacobas; Kamlesh U. Kukreja; Deborah A. Schady; Thuy Phung; Sridhar Sanvitha; Bindi J. Naik-Mathuria

doi:10.1089/lrb.2020.0004

Renal Lymphangiectasia in a Pediatric Patient

Sudhen B. Desai, Raphael C. Sun, Brittany L. Johnson, Kristy L. Rialon, Ionela Iacobas, Kamlesh U. Kukreja, Deborah A. Schady, Thuy Phung, Sridhar Sanvitha, Bindi J. Naik-Mathuria

Research output: Contribution to journal › Article › peer-review

1 Scopus citations

Abstract

Renal lymphatic abnormalities are rare, and the understanding of pathophysiology involving renal lymphatics is limited. Symptoms can include hypertension, hematuria, proteinuria, chyluria, and abdominal and lumbar pain. Imaging techniques specific to the renal lymphatics have not been clarified. We review the intrahospital imaging evaluation/workup and clinical course of a 6-year-old male who presented to our institution with a large perirenal cyst. His presentation presented a diagnostic and management challenge. The cyst was determined to be lymphatic in origin and required multiple interventional radiology and surgical procedures for management.

Original language	English (US)
Pages (from-to)	572-578
Number of pages	7
Journal	Lymphatic Research and Biology
Volume	18
Issue number	6
DOIs	https://doi.org/10.1089/lrb.2020.0004
State	Published - Dec 2020
Externally published	Yes

Keywords

Rapamycin
lymphangiectasia
lymphangiography
pediatric
renal cyst

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine

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10.1089/lrb.2020.0004

Cite this

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title = "Renal Lymphangiectasia in a Pediatric Patient",

abstract = "Renal lymphatic abnormalities are rare, and the understanding of pathophysiology involving renal lymphatics is limited. Symptoms can include hypertension, hematuria, proteinuria, chyluria, and abdominal and lumbar pain. Imaging techniques specific to the renal lymphatics have not been clarified. We review the intrahospital imaging evaluation/workup and clinical course of a 6-year-old male who presented to our institution with a large perirenal cyst. His presentation presented a diagnostic and management challenge. The cyst was determined to be lymphatic in origin and required multiple interventional radiology and surgical procedures for management.",

keywords = "Rapamycin, lymphangiectasia, lymphangiography, pediatric, renal cyst",

author = "Desai, {Sudhen B.} and Sun, {Raphael C.} and Johnson, {Brittany L.} and Rialon, {Kristy L.} and Ionela Iacobas and Kukreja, {Kamlesh U.} and Schady, {Deborah A.} and Thuy Phung and Sridhar Sanvitha and Naik-Mathuria, {Bindi J.}",

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doi = "10.1089/lrb.2020.0004",

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T1 - Renal Lymphangiectasia in a Pediatric Patient

AU - Desai, Sudhen B.

AU - Sun, Raphael C.

AU - Johnson, Brittany L.

AU - Rialon, Kristy L.

AU - Iacobas, Ionela

AU - Kukreja, Kamlesh U.

AU - Schady, Deborah A.

AU - Phung, Thuy

AU - Sanvitha, Sridhar

AU - Naik-Mathuria, Bindi J.

PY - 2020/12

Y1 - 2020/12

N2 - Renal lymphatic abnormalities are rare, and the understanding of pathophysiology involving renal lymphatics is limited. Symptoms can include hypertension, hematuria, proteinuria, chyluria, and abdominal and lumbar pain. Imaging techniques specific to the renal lymphatics have not been clarified. We review the intrahospital imaging evaluation/workup and clinical course of a 6-year-old male who presented to our institution with a large perirenal cyst. His presentation presented a diagnostic and management challenge. The cyst was determined to be lymphatic in origin and required multiple interventional radiology and surgical procedures for management.

AB - Renal lymphatic abnormalities are rare, and the understanding of pathophysiology involving renal lymphatics is limited. Symptoms can include hypertension, hematuria, proteinuria, chyluria, and abdominal and lumbar pain. Imaging techniques specific to the renal lymphatics have not been clarified. We review the intrahospital imaging evaluation/workup and clinical course of a 6-year-old male who presented to our institution with a large perirenal cyst. His presentation presented a diagnostic and management challenge. The cyst was determined to be lymphatic in origin and required multiple interventional radiology and surgical procedures for management.

KW - Rapamycin

KW - lymphangiectasia

KW - lymphangiography

KW - pediatric

KW - renal cyst

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Renal Lymphangiectasia in a Pediatric Patient

Abstract

Keywords

ASJC Scopus subject areas

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